TJ-CEO
2011 , Vol 6 , Num 3
Pseudoglaucomatous Cupping in A Young Adult with Cerebral Palsy/Periventricular Leukomalacia: A Brief Review of the Literature
1GATA Askeri Hastanesi, Göz Hastalıkları Anabilim Dalı Ankara, Uz. Dr.2GATA Askeri Hastanesi, Göz Hastalıkları Anabilim Dalı Ankara, Prof. Dr.
3GATA Askeri Hastanesi, Göz Hastalıkları Anabilim Dalı Ankara, Doç. Dr. Pseudoglaucomatous cupping of the optic disc can be the result of many ocular or nonocular conditions. Herein we report a young adult with a rare etiology of optic disc cupping. He was referred to our clinic for bilateral low vision. Ophthalmic examination revealed bilateral peripapillary atrophy, temporal pallor and excavation of the optic nerve head in his right eye. Intraocular pressure measurements at initial presentation and diurnal followup were within normal limits. Gonioscopy revealed bilateral open angles. Optic coherence tomography of optic discs revealed bilateral thinning of the retinal nerve fiber layer in the upper and upper temporal quadrants. On Heidelberg Retinal Tomography examination, topographic measurements were abnormal in his right eye. After performing standard automated perimetry we noticed a lower hemispheric visual field defect crossing the horizontal line and advancing to right upper quadrant in his both eyes. This type of a visual field defect evoked our suspicion about some kind of a central nervous system pathology. Neuroimaging revealed left periventricular (parietooccipital) and right occipital chronic infarction field consistent with the term “periventricular leukomalacia”. Keywords : Cerebral palsy, periventricular leukomalacia, pseudo-glaucomatous cupping, retrograde transsynaptic degeneration, temporal pallor